Respiratory involvement in juvenile dermatomyositis
نویسندگان
چکیده
Materials and methods 16 patients (9 girls) with diagnosis of JDM (age 3–16,2 yrs) performed pulmonary function tests (PFT). 14 were receiving treatment; all had muscular testing. 13 had weakness as major symptom. Respiratory symptoms: dry cough in 2/16; reduced exercise tolerance: 3/16. Chest xray: normal in 13/13. Echocardiogram and ECG: normal in all. 9/16 had positive ANA-Ab; antiJO1 Ab negative in all.
منابع مشابه
Non-Hodgkin lymphoma in a 13-year-old boy with provisional hypomyopathic juvenile Dermatomyositis
Provisional hypomyopathic juvenile dermatomyositis is a subgroup of clinically amyopathic juvenile dermatomyositis provisional. The diagnostic criteria include: Classic dermatomyositis skin lesions – which have to be confirmed by biopsy –, no involvement of proximal muscles, subclinical involvement of these muscles and normal level of muscle enzymes. These criteria should be present for a minim...
متن کاملLung involvement in rheumatologic diseases in children.
BACKGROUND Lung involvement in rheumatologic disease in children has been described with low frequency. OBJECTIVE To describe the lung function test and the radiological findings in a group of paediatric patients with rheumatologic diseases. METHODS Descriptive study. Pulmonary function was evaluated with spirometry, carbon monoxide diffusing capacity, blood arterial gas at rest and post ex...
متن کاملIdiopathic inflammatory myopathies and the lung.
Idiopathic inflammatory myositis (IIM) is a group of rare connective tissue diseases (CTDs) characterised by muscular and extramuscular signs, in which lung involvement is a challenging issue. Interstitial lung disease (ILD) is the hallmark of pulmonary involvement in IIM, and causes morbidity and mortality, resulting in an estimated excess mortality of 50% in some series. Except for inclusion ...
متن کاملOnset of juvenile dermatomyositis following varicella infection in a 12-month-old child: a case report
INTRODUCTION Infections can act as a trigger for juvenile dermatomyositis, with a predominance of respiratory tract infections reported previously. We present the first case of juvenile dermatomyositis following varicella infection to be described in the literature. CASE PRESENTATION A 15-month-old Caucasian girl was diagnosed with juvenile dermatomyositis 3 months after a varicella infection...
متن کاملFatal acute fibrinous and organizing pneumonia in a child with juvenile dermatomyositis.
Acute fibrinous and organizing pneumonia, a recently described form of diffuse acute lung injury, sometimes affects adults with inflammatory myopathy. We describe a child with juvenile dermatomyositis who had development of acute fibrinous and organizing pneumonia. There does not appear to be a successful method of treatment, particularly in severe cases with respiratory failure.
متن کامل